本帖最后由 pathology 于 2014-8-14 13:30 编辑
本周病例(2014.8.4—2014.8.10)
1、你考虑什么诊断?
胃丛状纤维粘液瘤(Gastric plexiform fibromyxoma)
胃丛状纤维粘液瘤又称为胃纤维粘液瘤(Gastric fibromyxoma)、丛状血管粘液样肌纤维母细胞肿瘤(Plexiform angiomyxoid myofibroblastic tumor)
Gastric plexiform fibromyxoma is a benign tumor recently added to the WHO Classification of Tumours of the Digestive System (IARC, 2010). It is considered rare and specific to the stomach. Most are multinoduar masses involving the muscularis propria or submucosa of the antral / prepyloric region, showing microscopically a multinodular proliferation of myofibroblastic cells and arborizing capillaries in a myxoid stroma. They have been seen over a broad age range. Metastases and recurrence following complete excision have not been described.
SMA
Desmin
CD117
CD34
S-100
Ki-67
2、需要做什么鉴别诊断?
炎性纤维**肉、粘液型胃肠道间质肿瘤、粘液型平滑肌瘤、神经鞘瘤、神经纤维瘤、韧带样纤维瘤病、炎性肌纤维母细胞瘤等
3、本病预后如何?
本病目前报道病例有限,倾向于良性或低度恶性肿瘤,完整手术局部切除即可。但其生物学行为尚需累积更多病例进一步研究观察。
Ref:
https://bbs.iiyi.com/thread-1988998-1.html
http://surgpathcriteria.stanford ... exiform-fibromyxoma
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本期病例比较少见但非常典型,结合临床病史、组织学形态,辅以免疫组化不难诊断。综合回答思路,rattlebox、molly011、fusuyong加一分,xhyong累积半分,maroaixb0079、派瑞松、jessayhome鲜花鼓励!
希望大家一如既往的支持病理每周一题,
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